The Impact of Diet on Body Composition in Patients with Maple Syrup Urine Disease

By:
Roberta Pretese, Cristina Bonfanti, Serena Gasperini, Martha Caterina Faraguna, Giulia Mezzanotti
Date:
2024
Resource type:
Blogs/news/opinion
Link:

This study examines the impact of a hypoproteic, semi-synthetic diet on the body composition of pediatric and adult patients with Maple Syrup Urine Disease (MSUD). Results show patients maintain healthy fat and lean mass but have a high prevalence of osteopenia. The findings highlight the diet's ability to stabilize metabolic conditions while posing risks to bone health, suggesting a need for targeted nutritional strategies and further research.

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